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Clinician orientation sheet

arr[GRCh38] 1q22(155454274_155539091)x1

Concise orientation only. Dates, normal findings, uncertainty, source boundaries, and longitudinal context remain in the complete profile.

Molecular result and profile context

Report genomic array result
arr[GRCh38] 1q22(155454274_155539091)x1
Affected ASH1L region
ASH1L exons 2–4 of 28 · NM_018489.3
Zygosity
Not stated
Molecular consequence
Intragenic copy-number deletion
Laboratory classification
Pathogenic
Classification source
Original report reviewed
Inheritance
De novo
Inheritance source
Family-confirmed parental testing
Genomic and gene-level notation
GRCh38 1q22:155454274–155539091 · ASH1L NM_018489.3 exons 2–4 of 28
Variant type
Deletion / CNV
Sex
Female
Age group
Ages 11–15
Protein position
No single protein position

Approved public summary

A girl in the 11–15 age group with a confirmed de novo pathogenic intragenic deletion affecting ASH1L exons 2–4. Her history includes intellectual disability, autism, delayed motor and language development, substantial communication and learning needs, childhood sleep and hearing difficulties, lifelong farsightedness and accommodative esotropia, tall stature with delayed skeletal maturation and pubertal development, genu valgum, bilateral hallux valgus requiring staged surgery, and scoliosis. She is also a future-minded young person who uses technology to communicate, continues building literacy and everyday skills, and talks about having a job and obtaining a driver’s licence.